Blastic Plasmacytoid Dendritic Cell Neoplasm Details

Expanded Description

A very rare aggressive cancer that usually manifests in skin lesions and infiltrates the lymph system. Usually considered a form of leukemia, it bears resemblances to lymphoma as well. Currently a chemotherapy regimen similar to that for AML followed by bone marrow/stem cell transplant seems to provide the best prognosis.

Because BPDCN is so rare, there are not sufficient data to give survival rates. Chemotherapy will often produce remission, but relapse rates were very high. Since 2006, the standard treatment has been a bone marrow transplant immediately after the first remission. This treatment has been successful, but there has not been enough time to accumulate 5-year survival rates with modern treatments.

Prevalence

0.0 ( Per 100,000 Population ) [Source]

Causes

No causes have been added yet.

Disorder Symptoms

No symptom information has been added yet.

We don't have any symptoms yet.

Diagnosis

No diagnosis information has been added yet.

Diagnostic Tests

No diagnostic test information has been added yet.

We don't have any tests yet.

Disorder Treatments

No treatment information has been added yet

We don't have any treatments yet.

Prognosis

Insufficient data with current treatments. Achieving remission through chemotherapy followed by a bone marrow or stem cell transplant immediately after the first remission seems to offer the best prognosis.

Tips for Living with the Disorder

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