Scleromyxedema Details

Expanded Description

Scleromyxedema is a condition of mucinous deposition in the skin associated with monoclonal gammopathy characterized by a flesh-colored, papular skin eruption. The average age onset is 55 years and there was roughly equal distribution of gender.

As the disease progresses, mucin deposition progresses to internal organs, joints, and connective tissues thus leading to “stiff man” like scleroderma. As things progress, internal problems can go into the brain and vital organs with bad results.

Prevalence

150.0 ( Cases ) [Source]

Causes

The cause of Scleromyxedema is unknown, but is most probably autoimmune.

Disorder Symptoms

No symptom information has been added yet.

We don't have any symptoms yet.

Diagnosis

No diagnosis information has been added yet.

Diagnostic Tests

Deep tissue biopsy and bone marrow biopsy. A skin biopsy is much less invasive.

We don't have any tests yet.

Disorder Treatments

IVIg

Name
Intravenous Immunoglobulin

Prognosis

Current prognosis is poor, but there is more hope with the IVIg treatment.

Tips for Living with the Disorder

We don't have any tips yet.